Meningiomatosis in a patient with no family history that conditions the development of the disease
Keywords:
meningiomatosis, multiple meningioma, neurofibromatosis type 2.Abstract
Introduction: Meningiomas are tumors that originate from the meninges. These constitute the most common extra-axial intracranial tumors, generally benign and slow growing. Multiple meningiomas are considered when a patient without neurofibromatosis type 2 has more than one meningioma within the central nervous system, regardless of whether they occur simultaneously or separately in time.
Objective: To describe clinical and imaging aspects of meningiomatosis in a patient with no family history that determines the development of the disease.
Case report: This the case of a white female patient, 68 years old, with history of compensated ischemic heart disease and high blood pressure, and no family history of other diseases. Approximately seven months ago, she began to report progressive weakness and instability at walking, with tendency to lateralize to the right. These symptoms were associated with oppressive headache in the right hemicranial zone with no other clinical elements. Simple and contrasted cranial magnetic resonance imaging confirmed the presence of multiple brain meningiomas.
Conclusion: The imaging studies, the age of presentation in the absence of criteria and family history of neurofibromatosis type 2 or another genetic disease that determines the development of meningiomatosis, made it possible to diagnose multiple, probably sporadic, meningiomas in the case reported.
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